Abstract
We report a known case of thalassemia intermedia (Hb Dhofar) who in spite of mild thalassemic facies, attained his normal genetic height, pubertal maturity and improved self-image with minimal splenomegaly through a hypertransfusion/chelation regimen that was started just before puberty and maintained for 5 years. As there are no clear guidelines in the management of patients with thalassemia intermedia, the option of hypertransfusion/chelation during the pubertal growth spurt may alleviate some of the complications associated with thalassemia intermedia.
Keywords
Publication details
- DOI
- 10.5001/omj.2012.125
- Journal
- Oman Medical Journal
- Publisher
- Oman Medical Specialty Board
- Open access
- Gold open access
Cite this article
APA 7
Tony, S., Daar, S., Zachariah, M., & Wali, Y. (2012). Prepubertal Hypertransfusion in Thalassemia Intermedia: Sustained Positive Effects on Growth, Splenic Function and Endocrine Parameters. Oman Medical Journal. https://doi.org/10.5001/omj.2012.125
MLA 9
Tony, Surekha, et al. "Prepubertal Hypertransfusion in Thalassemia Intermedia: Sustained Positive Effects on Growth, Splenic Function and Endocrine Parameters." Oman Medical Journal, 2012. https://doi.org/10.5001/omj.2012.125.
Chicago (author–date)
Tony, Surekha, Shahina Daar, Mathew Zachariah, and Yasser Wali. 2012. "Prepubertal Hypertransfusion in Thalassemia Intermedia: Sustained Positive Effects on Growth, Splenic Function and Endocrine Parameters." Oman Medical Journal. https://doi.org/10.5001/omj.2012.125.
Harvard
Tony, S., Daar, S., Zachariah, M. and Wali, Y. (2012) 'Prepubertal Hypertransfusion in Thalassemia Intermedia: Sustained Positive Effects on Growth, Splenic Function and Endocrine Parameters', Oman Medical Journal. doi:10.5001/omj.2012.125.
Vancouver
Tony S, Daar S, Zachariah M, Wali Y. Prepubertal Hypertransfusion in Thalassemia Intermedia: Sustained Positive Effects on Growth, Splenic Function and Endocrine Parameters. Oman Medical Journal. 2012. doi:10.5001/omj.2012.125
IEEE
S. Tony, S. Daar, M. Zachariah, and Y. Wali, "Prepubertal Hypertransfusion in Thalassemia Intermedia: Sustained Positive Effects on Growth, Splenic Function and Endocrine Parameters," Oman Medical Journal, 2012, doi: 10.5001/omj.2012.125.