Abstract

Hypocomplementemic urticarial vasculitis syndrome is an immune complex-mediated disease of unknown etiology. The clinical course is characterized by urticaria, conjunctivitis, joint pain, and hypocomplementemia. We here report a case of a child with hypocomplementemic urticarial vasculitis syndrome that progressed to nephritis. Renal biopsy was consistent with diffuse proliferative glomerulonephritis with diffuse subendothelial immune deposits. He responded well to a combination of steroid and mofetil micofenolate.

Keywords

Publication details

DOI
10.5001/omj.2013.76
Journal
Oman Medical Journal
Publisher
Oman Medical Specialty Board
Open access
Gold open access

Cite this article

APA 7

Al Mosawi, Z. S. A., & Al Hermi, B. E. A. (2013). Hypocomplementemic Urticarial Vasculitis Syndrome in an 8-year-old Boy: A Case Report and Review of Literature. Oman Medical Journal. https://doi.org/10.5001/omj.2013.76

MLA 9

Al Mosawi, Zakiya Saleh Adnan, and Badriya Ebrahim Ahmed Al Hermi. "Hypocomplementemic Urticarial Vasculitis Syndrome in an 8-year-old Boy: A Case Report and Review of Literature." Oman Medical Journal, 2013. https://doi.org/10.5001/omj.2013.76.

Chicago (author–date)

Al Mosawi, Zakiya Saleh Adnan, and Badriya Ebrahim Ahmed Al Hermi. 2013. "Hypocomplementemic Urticarial Vasculitis Syndrome in an 8-year-old Boy: A Case Report and Review of Literature." Oman Medical Journal. https://doi.org/10.5001/omj.2013.76.

Harvard

Al Mosawi, Z. S. A. and Al Hermi, B. E. A. (2013) 'Hypocomplementemic Urticarial Vasculitis Syndrome in an 8-year-old Boy: A Case Report and Review of Literature', Oman Medical Journal. doi:10.5001/omj.2013.76.

Vancouver

Al Mosawi ZSA, Al Hermi BEA. Hypocomplementemic Urticarial Vasculitis Syndrome in an 8-year-old Boy: A Case Report and Review of Literature. Oman Medical Journal. 2013. doi:10.5001/omj.2013.76

IEEE

Z. S. A. Al Mosawi, and B. E. A. Al Hermi, "Hypocomplementemic Urticarial Vasculitis Syndrome in an 8-year-old Boy: A Case Report and Review of Literature," Oman Medical Journal, 2013, doi: 10.5001/omj.2013.76.