Abstract

Ewing sarcoma is one of the rare, highly malignant neuroectodermal tumors frequently involving bones. Primary orbital Ewing sarcoma is extremely uncommon. We report a rare case of a 5-year-old boy who presented to us with a painless, slow-growing mass above the medial canthus of the left eye, the clinical appearance of which was masquerading as an internal angular dermoid. The child was subsequently diagnosed to have primary orbital Ewing sarcoma. Primary orbital Ewing sarcoma is a rare tumor with poor prognosis, poses diagnostic challenges, and demands a high index of clinical suspicion.

Keywords

Publication details

DOI
10.4103/ojo.ojo_180_21
Journal
Oman Journal of Ophthalmology, 15(2), 228-230
Publisher
Medknow Publications
Open access
Gold open access

Cite this article

APA 7

Mendonca, T. M., Lashkari, H. P., Suresh, P. K., Kondaveti, R., Ali, F., & Rodrigues, G. R. (2022). Wolf in sheep's clothing: Primary orbital Ewing sarcoma in a child masquerading as internal angular dermoid. Oman Journal of Ophthalmology, 15(2), 228-230. https://doi.org/10.4103/ojo.ojo_180_21

MLA 9

Mendonca, Teena Mariet, et al. "Wolf in sheep's clothing: Primary orbital Ewing sarcoma in a child masquerading as internal angular dermoid." Oman Journal of Ophthalmology, vol. 15, no. 2, 2022, pp. 228-230. https://doi.org/10.4103/ojo.ojo_180_21.

Chicago (author–date)

Mendonca, Teena Mariet, Harsha Prasada Lashkari, Pooja K Suresh, Rahul Kondaveti, Faraz Ali, and Gladys R Rodrigues. 2022. "Wolf in sheep's clothing: Primary orbital Ewing sarcoma in a child masquerading as internal angular dermoid." Oman Journal of Ophthalmology 15 (2): 228-230. https://doi.org/10.4103/ojo.ojo_180_21.

Harvard

Mendonca, T. M., Lashkari, H. P., Suresh, P. K., Kondaveti, R., Ali, F. and Rodrigues, G. R. (2022) 'Wolf in sheep's clothing: Primary orbital Ewing sarcoma in a child masquerading as internal angular dermoid', Oman Journal of Ophthalmology, 15(2), pp. 228-230. doi:10.4103/ojo.ojo_180_21.

Vancouver

Mendonca TM, Lashkari HP, Suresh PK, Kondaveti R, Ali F, Rodrigues GR. Wolf in sheep's clothing: Primary orbital Ewing sarcoma in a child masquerading as internal angular dermoid. Oman Journal of Ophthalmology. 2022;15(2):228-230. doi:10.4103/ojo.ojo_180_21

IEEE

T. M. Mendonca, H. P. Lashkari, P. K. Suresh, R. Kondaveti, F. Ali, and G. R. Rodrigues, "Wolf in sheep's clothing: Primary orbital Ewing sarcoma in a child masquerading as internal angular dermoid," Oman Journal of Ophthalmology, vol. 15, no. 2, pp. 228-230, 2022, doi: 10.4103/ojo.ojo_180_21.