Abstract

Retinal vascular occlusions are rare in young people, and any occlusion warrants an extensive clinical evaluation to establish the etiology. Cardiac malformations are a source of embolism. We present a case of atrial septal defect (ASD) in a patient with type II Mayer-Rokitansky-Küster-Hauser syndrome, leading to unilateral branch retinal arterial occlusion (BRAO) in a young woman. A 21-year-old woman presented with sudden, painless, blurring of vision, and a superior visual field defect in her right eye. A fundus examination confirmed the BRAO diagnosis. Ocular and systemic evaluation revealed primary amenorrhea, ASD, ectopic kidneys, and pelvic cyst. Any vascular occlusion in a young patient must be thoroughly evaluated, including a detailed systemic history.

Keywords

Publication details

DOI
10.4103/ojo.ojo_48_24
Journal
Oman Journal of Ophthalmology, 17(3), 393-395
Publisher
Medknow Publications
Open access
Gold open access

Cite this article

APA 7

Bedwal, A., Banerjee, M., & Rewri, P. (2024). Branch retinal artery occlusion in a young patient with Mayer-Rokitansky-Küster-Hauser type 2 syndrome. Oman Journal of Ophthalmology, 17(3), 393-395. https://doi.org/10.4103/ojo.ojo_48_24

MLA 9

Bedwal, Anita, et al. "Branch retinal artery occlusion in a young patient with Mayer-Rokitansky-Küster-Hauser type 2 syndrome." Oman Journal of Ophthalmology, vol. 17, no. 3, 2024, pp. 393-395. https://doi.org/10.4103/ojo.ojo_48_24.

Chicago (author–date)

Bedwal, Anita, Mousumi Banerjee, and Parveen Rewri. 2024. "Branch retinal artery occlusion in a young patient with Mayer-Rokitansky-Küster-Hauser type 2 syndrome." Oman Journal of Ophthalmology 17 (3): 393-395. https://doi.org/10.4103/ojo.ojo_48_24.

Harvard

Bedwal, A., Banerjee, M. and Rewri, P. (2024) 'Branch retinal artery occlusion in a young patient with Mayer-Rokitansky-Küster-Hauser type 2 syndrome', Oman Journal of Ophthalmology, 17(3), pp. 393-395. doi:10.4103/ojo.ojo_48_24.

Vancouver

Bedwal A, Banerjee M, Rewri P. Branch retinal artery occlusion in a young patient with Mayer-Rokitansky-Küster-Hauser type 2 syndrome. Oman Journal of Ophthalmology. 2024;17(3):393-395. doi:10.4103/ojo.ojo_48_24

IEEE

A. Bedwal, M. Banerjee, and P. Rewri, "Branch retinal artery occlusion in a young patient with Mayer-Rokitansky-Küster-Hauser type 2 syndrome," Oman Journal of Ophthalmology, vol. 17, no. 3, pp. 393-395, 2024, doi: 10.4103/ojo.ojo_48_24.