الملخص
Hereditary haemorrhagic telangiectasia (HHT) is an autosomal dominant disorder characterised by vascular dysplasia. Hepatic vascular m alformations (VMs) range from small telangiectases to significant vascular shunting. Here we report two cases of HHT. Case 1 had diffuse ectasia of the hepatic artery along its intrahepatic and extrahepatic course with a hepatic arterial aneurysm. Case 2 presented with ileal and hepatic telangiectases. Knowledge of these vascular variants is indispensable for clinicians and radiologists in aiding diagnosis and surgical and interventional management.
بيانات النشر
- المعرّف الرقمي
- 10.18295/squmj.1.2023.011
- المجلة
- مجلة جامعة السلطان قابوس الطبية, 23(4), 551-555
- الناشر
- جامعة السلطان قابوس
- وصول مفتوح
- وصول مفتوح ذهبي
- الترخيص
- CC BY-ND 4.0
اقتبس هذه المقالة
APA 7
Alagappan, A., Sahoo, B., Prakash, J. H., Panigrahi, M. K., & Tripathy, T. (2025). Hepatic Vascular Variants in Hereditary Haemorrhagic Telangiectasia: Imaging findings. Sultan Qaboos University Medical Journal, 23(4), 551-555. https://doi.org/10.18295/squmj.1.2023.011
MLA 9
Alagappan, Alamelu, et al. "Hepatic Vascular Variants in Hereditary Haemorrhagic Telangiectasia: Imaging findings." Sultan Qaboos University Medical Journal, vol. 23, no. 4, 2025, pp. 551-555. https://doi.org/10.18295/squmj.1.2023.011.
شيكاغو (المؤلف–التاريخ)
Alagappan, Alamelu, Biswajit Sahoo, Jain H. Prakash, Manas K. Panigrahi, and Taraprasad Tripathy. 2025. "Hepatic Vascular Variants in Hereditary Haemorrhagic Telangiectasia: Imaging findings." Sultan Qaboos University Medical Journal 23 (4): 551-555. https://doi.org/10.18295/squmj.1.2023.011.
هارفارد
Alagappan, A., Sahoo, B., Prakash, J. H., Panigrahi, M. K. and Tripathy, T. (2025) 'Hepatic Vascular Variants in Hereditary Haemorrhagic Telangiectasia: Imaging findings', Sultan Qaboos University Medical Journal, 23(4), pp. 551-555. doi:10.18295/squmj.1.2023.011.
فانكوفر
Alagappan A, Sahoo B, Prakash JH, Panigrahi MK, Tripathy T. Hepatic Vascular Variants in Hereditary Haemorrhagic Telangiectasia: Imaging findings. Sultan Qaboos University Medical Journal. 2025;23(4):551-555. doi:10.18295/squmj.1.2023.011
IEEE
A. Alagappan, B. Sahoo, J. H. Prakash, M. K. Panigrahi, and T. Tripathy, "Hepatic Vascular Variants in Hereditary Haemorrhagic Telangiectasia: Imaging findings," Sultan Qaboos University Medical Journal, vol. 23, no. 4, pp. 551-555, 2025, doi: 10.18295/squmj.1.2023.011.