[
    {
        "id": "osp-2671",
        "type": "article-journal",
        "title": "Rare Congenital Dissecting Thoracic Aortic Aneurysm in a Child with Noonan Syndrome: A Case Report",
        "author": [
            {
                "family": "Maulana",
                "given": "Siti Aishah Ahmad"
            },
            {
                "family": "Alwi",
                "given": "Sharifah Huda Engku"
            },
            {
                "family": "Hashim",
                "given": "Mohd Shafie"
            },
            {
                "family": "Rohim",
                "given": "Rabiatul Adawiyah Abdul"
            }
        ],
        "URL": "https://omanscience.com/en/articles/rare-congenital-dissecting-thoracic-aortic-aneurysm-in-a-child-with-noonan-syndrome-a-case-report",
        "language": "en",
        "issued": {
            "date-parts": [
                [
                    2023
                ]
            ]
        },
        "container-title": "Oman Medical Journal",
        "DOI": "10.5001/omj.2023.66",
        "publisher": "Oman Medical Specialty Board",
        "ISSN": "1999-768X",
        "abstract": "We present a rare case of congenital thoracic aortic aneurysm (TAA) complicated with dissection in a nine-year-old girl with Noonan syndrome and atrial septal defect. She presented with rapid breathing and upper respiratory tract symptoms. Chest X-ray revealed a huge upper mediastinum with cardiomegaly. Echocardiogram showed possible ascending TAA. Computerized tomography angiogram of the aorta revealed huge aortic root-ascending TAA with small aortic dissection. Despite immediate treatment, the patient passed away due to severe airway compromise."
    }
]