[
    {
        "id": "osp-10100",
        "type": "article-journal",
        "title": "Paediatric Restrictive Cardiomyopathy - Diagnosis and Challenges: A report of two cases",
        "author": [
            {
                "family": "Husain",
                "given": "Dalal S."
            },
            {
                "family": "Joshi",
                "given": "Niranjan P."
            },
            {
                "family": "Al Senaidi",
                "given": "Khalfan S."
            },
            {
                "family": "Al Riyami",
                "given": "Hilal"
            }
        ],
        "URL": "https://omanscience.com/en/articles/paediatric-restrictive-cardiomyopathy-diagnosis-and-challenges-a-report-of-two-cases",
        "language": "en",
        "issued": {
            "date-parts": [
                [
                    2025
                ]
            ]
        },
        "container-title": "Sultan Qaboos University Medical Journal",
        "volume": "24",
        "issue": "2",
        "page": "283-287",
        "DOI": "10.18295/squmj.9.2023.055",
        "publisher": "Sultan Qaboos University",
        "ISSN": "2075-051X",
        "abstract": "Restrictive cardiomyopathy is one of the rarest forms of cardiomyopathies in paediatric patients characterised by impaired myocardial relaxation or compliance with restricted ventricular filling, leading to a reduced diastolic volume with a preserved systolic function. We report 2 cases—a 5-year-old boy who presented with abdominal distension and palpitation with family history of similar complaints but no definite genetic diagnosis as yet and a 5-year-old girl who presented with chronic cough and shortness of breath. Both cases were diagnosed in a tertiary care hospital in Muscat, Oman, in 2019 and are managed supportively with regular outpatient follow-up. This is the first series of reported cases of paediatric restrictive cardiomyopathy from Oman.\n\nKeywords: Cardiomyopathy; Restrictive Cardiomyopathy; Congestive Heart Failure."
    }
]